Inherited disorder , autosomal dominant inheritance pattern .
Local manifestation: cafe-au-lait spots, pigmented nevi, axillary freckling. slow growing cutaneous and subcutaneous neurofibromas.
Symptomatic treatment of assessed manifestation ( seizures, skeleton defects ; scoliosis, kyposis) and surgical removal of troublesome tumors
Refer to support groups, family needs to know about genetic implications
Hockenberry, 2009, Wong’s essentials of pediatric nursing, 8th edition. Mosby.